En coup de sabre — a case report of therapeutic difficulties


morpheaen coup de sabre
triamcinolone morphea typu cięcia szablą

How to Cite

Szymoniak-Lipska M, Cieplewicz P, Polańska A, Żaba R, Adamski Z, Dańczak-Pazdrowska A. En coup de sabre — a case report of therapeutic difficulties. JoFA [Internet]. 2020Dec.31 [cited 2022May17];3(2):139-44. Available from: http://jofa.ump.edu.pl/index.php/jofa/article/view/39


En coup de sabre (ECDS) is a rare linear form of localized scleroderma that occurs more frequently in children than in adults. The involvement of the scalp leads to cicatricial alopecia. The aim of this paper is to present a problematic case of ECDS in young female patient. Many terapeutical methods were introduced, based on guidelines described in diagnostic and therapeutic recommendations of the Polish Dermatological Society (e.g. methotrexate, oral and intravenous glucocorticoids, subcutaneous triamcinolone injections and topical high potent steroids as well as kalcineurin inhibitor (tacrolimus). The lasting improvement was not achieved. The remission was finally induced after the implementation of mycophenolate mofetil.



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